Fig. 2

Genealogical tree. Square: males; circles: females. Renal US normal at 65 years (I.1); renal US normal at 66 years (I.2); renal US normal at 42 years (II.1); renal US normal at 18 and 12 years (III.3 & III.4, respectively); 2 years old, ADPKD screening not performed (IV-1)